2026-05-09T21:22:01Z https://www.peertechzpublications.org/oai-pmh

oai:www.peertechzpublications.org:10.17352/jgro.000130 2024-12-24 PTZ.JGRO:VOL10

Prune Belly Syndrome: A Special Case G Bassir I Maali A Gotni A Assal M Bensouda M Jalal A LamrissiN Samouh<p>Prune Belly Syndrome (PBS) is an extremely rare anatomo-radiological syndrome that combines aplasia of the muscles of the anterior wall of the abdomen, dilatations of the urinary tract, and testicular malformations, forming the classic triad of the syndrome. However, up to 75% of patients with PBS present with pulmonary, skeletal, cardiac, and gastrointestinal malformations. We report the case of a male neonate born at term to a mother with no particular pathological history, in whom the clinical examination at birth revealed hypoplasia of the muscles of the anterior abdominal wall and congenital dislocation of the hip. Hypoplasia of the abdominal wall muscles was confirmed by abdominal ultrasound and abdominal CT scan, and cardiac malformations were also found on transthoracic ultrasound. The outcome can vary widely, from stillbirth due to major renal and respiratory dysplasia to a virtually normal child. All this explains the great diversity of opinions on the attitude to adopt when faced with this syndrome.</p> Journal of Gynecological Research and Obstetrics - Peertechz Publications 2024-12-24 Case Report https://doi.org/10.17352/jgro.000130 en Copyright © G Bassir et al.